2021, Vol. 4, Issue 3, Part C
Anaesthetic management of a infant with Pierre robin sequence
Author(s): Dr. Niranjni S, Dr. Harish Kumar J and Dr. Lakshmi
Abstract: Pierre Robin sequence (PRS) is characterized by the clinical triad of micrognathia (small mandible), glossoptosis (backward, downward displacement of the tongue), U or V shaped cleft palate and airway obstruction defines the Pierre Robin sequence (PRS). Airway obstruction and respiratory distress are clinical hallmarks. It occurs in 1:8500 live births with an equal male-to-female ratio. The mechanical theory which states that initiating event is mandibular hypoplasia which keeps the tongue high within the oral cavity; this in turn causes a cleft palate by preventing the closure of the palatal shelves, this syndrome is now called as Pierre robin sequence. These cases pose a challenge to the anesthetist as they present at a very young age, may have associated congenital anomalies, varying degrees of difficult airway, need repeated corrective surgeries, and lastly the airway has to be shared with the surgeons.
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How to cite this article:
Dr. Niranjni S, Dr. Harish Kumar J, Dr. Lakshmi. Anaesthetic management of a infant with Pierre robin sequence. Int J Med Anesthesiology 2021;4(3):169-171. DOI: 10.33545/26643766.2021.v4.i3c.300